The cause may be one of the following:
  • Family history of PAH (familial or heritable PAH)
  • PAH associated with another disease or condition that a person already has (examples include connective tissue diseases, such as scleroderma; HIV; and exposures to certain drugs or toxins)
  • Idiopathic PAH for which no specific cause or risk factor can be identified

The 6-minute walk test is used to measure how far you can walk in 6 minutes.

Usually your regular doctor will refer you to a cardiologist or pulmonologist. There are also doctors who specialize in treating PAH and can be found at PH Care Centers.

Currently, there are 14 FDA-approved medications on the market, with more in development. United Therapeutics offers 4 treatment options for PAH: 3 prostacyclin analogues and 1 PDE-5 inhibitor.

Talk to your doctor about the best treatment options for you based on your symptoms and clinical evaluation performed at each checkup. PAH is a progressive disease so your doctor will continue to evaluate you for signs of progression that may warrant a change in treatment.

It is important to talk to your doctor about how you are feeling and set goals to ensure you are getting the most out of your treatment.

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