Glossary of terms

6-minute walk test: A test that tracks how far you can walk in 6 minutes.

Analogue: A synthetic medication that is designed to be structurally similar to a natural substance and to act similarly in the body.

BNP levels: High levels of b-type natriuretic peptide indicate too much strain on your heart, or even heart failure.

Echocardiogram: An ultrasound that is used to check the size and function of the right side of your heart.

Endothelin: 1 of the 3 natural substances in your body that is impacted by PAH; helps increase blood pressure and makes blood vessels firm when needed.

Functional class (FC): A system of 4 classes created by the World Health Organization to assess the severity of symptoms in patients with PAH.

Nitric oxide: 1 of the 3 natural substances in your body that is impacted by PAH; helps control blood pressure by opening arteries when needed.

Prostacyclin: 1 of the 3 natural substances in your body that is impacted by PAH; it helps the blood vessels in your lungs stay open and makes it easier for your heart to pump fresh, oxygenated blood to the lungs.

Pulmonary arterial hypertension (PAH): A chronic and progressive rare disease that affects your heart's ability to pump blood to your lungs.

Pulmonary function test (PFT): A test that measures your lung function.

Right heart catheterization: The only test that can confirm a PAH diagnosis; measures the pressure in your heart and the arteries in your lung.

Specialty Pharmacy Services (SPS): Pharmacies that provide personalized care and are different from your local pharmacy.

Ventilation/Perfusion scan: A test that measures your breathing and circulation in your lungs.